Partial anomalous pulmonary venous drainage (PAPVD) is a rare congenital cardiac defect and is associated with sinus venosus atrial septal defect. While most cases are asymptomatic, a patient can present with pulmonary hypertension (PHTN) and it can be difficult to diagnose. Here, we discuss the case of a young female with PHTN who was found to have two right-sided PAPVD. Through this case, authors try to emphasize the importance of meticulous and thorough investigation when evaluating PHTN, which allows for correct diagnosis and a timely intervention before PHTN becomes irreversible.
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Recommended CitationPatel, Hiten R.; Bhutani, Suchit; Shamoon, Fayez; and Virk, Hartaj, "Deciphering a case of pulmonary hypertension in a young female: Partial anomalous pulmonary venous drainage the culprit" (2018). Abington Jefferson Health Papers. Paper 1.