AL amyloidosis is a rare disease, with only 1200-3200 new cases in the US per year.1 Two-thirds of patients are male; presentation typically occurs after age fifty.1,2,3 Amyloid can involve the kidneys (74%), heart (60-90%), liver (27%), peripheral nervous system (22%), and carpal tunnel (20%).3 We describe an atypical presentation of AL amyloidosis and highlight the importance of recognizing this disease in patients with systemic signs.
Kujawski, MS3, Brandon; Johnson, MS3, Drew; Radadia, MS4, Kushan; Feduska, MD, Eric; Ford, MD, Robert; Uppal, MD, Guldeep; Kabir, MD, PhD, Mariam; and Stewart, MD, John
"An Uncommon Presentation of Amyloidosis,"
The Medicine Forum:
Vol. 15, Article 5.
Available at: http://jdc.jefferson.edu/tmf/vol15/iss1/5